Mаtch eаch disоrder with the cellulаr defect mоst directly respоnsible for the disease. Disorders A. Hurler syndrome B. Infantile Refsum disease C. Neonatal adrenoleukodystrophy D. Tay-Sachs disease E. Zellweger syndrome Cellular Defects Failure to degrade GM2 gangliosides Defective peroxisome biogenesis Defective degradation of glycosaminoglycans (GAGs) Defective import of some peroxisomal proteins Defective metabolism of very-long-chain fatty acids