A 3-yeаr-оld bоy is brоught to the pediаtriciаn’s office for an ear infection. He has had recurrent respiratory, ear, and skin bacterial infections since 6 months of age. He has required inpatient admissions to the pediatric ward four times for intravenous antibiotics. On physical exam, he has no tonsils and has no history of tonsillectomy. Levels of IgG, IgM, and IgA are decreased. Decrease count of B cells, T cell count is normal. His oral exam is shown below. Genetic testing is sent to confirm the diagnosis. What is the most likely diagnosis?